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Pol. Merkur. Lek (Pol. Med. J.), 2016, XL/236: 110-112 Maximize

Pol. Merkur. Lek (Pol. Med. J.), 2016, XL/236: 110-112

Title: Neurologic appearence of Behçet disease in 14-year old boy treated with adalimumab with good result 

Authors: Iwańczak B, Reich A, Kofla-Dłubacz A, Kazanowska B, Ruczka M 

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SUMMARY IN POLISH & ENGLISH. FULL ARTICLE ONLY IN POLISH.

Neurologic appearence of Behçet disease in 14-year old boy treated with adalimumab with good result


Iwańczak B1, Reich A2, Kofla-Dłubacz A1, Kazanowska B3, Ruczka M.1

Medical University of Wrocław, Poland: 12nd Department and Clinic of Pediatrics, Gastroenterology and Nutrition; 2Department of Dermatology, Venerology and Allergology; 3Department and Clinic of Pediatric Oncology, Haematology and Bone Marrow Transplantation

Behçet disease is a multiorgan inflammatory vessel disorder of unknown etiology which only occasionally occurs in children. Here, we demonstrate a 14-year-old boy with Behçet disease diagnosed based on recurrent aphthous stomatitis, acneiform facial lesions, subpreputial erosions and extensive thrombosis involving sigmoid sinus, transverse sinus and right internal cervical vein. Treatment with low molecular weight heparins, systemic corticosteroids, and azathioprine only resulted in partial remission of clinical symptoms. Addition of adalimumab led to complete resolution of clinical and biochemical abnormalities and disappearance of thrombosis in central nervous system.

Key words: Behçet disease, neurological form, children

Pol Med J, 2016; XL (236); 110–112